Nursing care
This is the priority respiratory intervention with patient's with CF
Mobilize secretions
Mucolytic used to thin secretions in cystic fibrosis
Dornase alfa (pulmozyme)
The sound auscultated when air is moving through a narrowed airway
Wheezing
True or false: It is possible to reverse airway obstruction resulting from asthma
True
This color-coded tool helps families manage asthma at home and know when to seek care
Asthma action plan
Children with cystic fibrosis require this dietary modification.
High calorie, high protein diet with unrestricted fat.
First line rescue medication for asthma exacerbation
Albuterol
This device can be used to monitor lung function in clients with asthma
Peak flow meter
This non-invasive test is used to confirm the diagnosis of cystic fibrosis
Sweat chloride test
What’s the first action a nurse should take if a child is using a peak flow meter and the result is in the red zone?
Administer a rescue inhaler
Airway clearance techniques
The nurse monitors this lab value for the child receiving methylprednisolone for an asthma exacerbation
Glucose
Common symptom of CF in the newborn
Constipation/meconium ileus, salty tasting skin
Cystic fibrosis follows this inheritance pattern
Autosomal recessive
Cystic fibrosis primarily affects these 2 body systems.
Respiratory and gastrointestinal
True or false: The nurse should advise the client with exercise induced asthma to avoid strenuous exercise
False
Pancrelipase is administered at this time
This vital sign is particularly important to monitor in a patient with an asthma exacerbation?
Respiratory rate
Serious complication that can arise from overuse of short acting beta-agonists
Status asthmaticus
Children with CF require supplementation of these vitamins.
A, D, E, K
In addition to short acting beta agonists and systemic corticosteroids, this is a priority intervention for the client in status astmaticus
High flow oxygen, inhaled anticholinergics
True or false: Oral steroids are a type of long term/controller medication for clients with asthma
False
Clubbing in a client with cystic fibrosis indicates this complication
Chronic hypoxia
Common metabolic condition that arises from pancreatic insufficiency in clients with CF, typically presenting in the 3rd decade of life
Cystic fibrosis related diabetes (CFRD)
Children with CF are at increased risk for lung infections due to this
Thick mucous that traps bacteria in the lungs