Anatomy
This defect is one of the most common cyanotic defects and is characterized by ventricular discordance
What is d-TGA?
Great vessels arise from the incorrect ventricles
In this defect, there is complete intracardiac mixing of systemic and pulmonary venous return, with resultant low sats and is caused by a common trunk consisting of pulmonary artery and aorta.
What is truncus arteiosus?
In d-TGA, the heart has otherwise normal connections. This anatomy results in a ________ circulation
(parallel or series)
What is parallel?
This is known as an extreme version of coarctation of the aorta and a discontinuity between the ascending and descending aorta.
What is interrupted aortic arch (IAA)?
All of the pulmonary veins connect abnormally to the heart.
What is total anomalous venous return (TAPVR)?
There are various forms but all involve oxygenated blood from lungs being carried by pulmonary veins back to the right side of the heart instead of the left atrium.
This is the first surgery to palliate HLHS.
What is a Norwood procedure?
It creates a neo-aorta as well as atrial septectomy to allow mixing of blood
This defect is characterized by both ventricular discordance as well as atrioventricular discordance.
What is l-TGA?
The left-sided morphologic RV is responsible for systemic blood flow
Prior to ductal closure, infants have normal O2 sats in the upper body and deoxygenated blood in the lower body with differential cyanosis
What is interrupted aortic arch (IAA)?
In l-TGA, there is ventriculoarterial discordance as well as atrioventricular discordance. This results in ________ circulation.
parallel or series
What is series circulation?
In this defect, the left ventricle is underdeveloped as well as many or all left side structure of the heart.
What is hypoplastic left heart syndrome (HLHS)
The repair of this defect involves emoval of pulmonary arteries from arterial trunk so aorta provides only systemic flow
What is truncus arteriosus?
This defect cannot be repaired but is palliated so that the heart functions as a single ventricle.
What is hypoplastic left heart (HLHS)?
This palliative surgery involves dividing the SVC and connecting it to the right pulmonary artery
What is the bidirectional Glenn?
This allows deoxygenated blood from the head and neck to flow directly to the pulmonary arteries.
The IVC is connected to the pulmonary artery via a surgically created tunnel in this procedure.
What is the Fontan procedure?
This device can be used as a bridge to heart transplant or a method to allow the heart to heal after infection or trauma.
What is an Left ventricular device (LVAD)?