CF Basics & Diagnosis
Cystic fibrosis is...
What is a genetic disorder affecting the exocrine glands?
This causes blocked airways in CF.
What is thick, sticky mucous?
This organ’s duct is blocked, leading to malabsorption
What is the pancreas?
This is CF effect on sweat
What is salty sweat?
This supplement CF patients must take with every meal
What are pancreatic enzymes?
The main characteristic of mucus in CF patients.
What is thick and sticky?
This common sign occurs in the fingers due to chronic low oxygen.
What is clubbing of the nails?
These three enzymes are blocked from reaching the intestine in CF.
What are protease, amylase, and lipase? (PAL)
This is used to stimulate sweat for testing
What is pilocarpine?
You should never do this to pancreatic enzyme capsules
What is chew or crush them?
Systems that are most affected by CF
What are the respiratory, digestive, integumentary, and reproductive systems?
Name one bacteria CF patients often get infected with.
What is Pseudomonas aeruginosa or Staphylococcus aureus?
This type of stool is what CF patients have without pancreatic enzymes.
What is greasy and odorous stool?
This chloride level is inconclusive for CF
What is 40–59 mmol/L?
Name two types of respiratory medications used for CF.
What are bronchodilators and mucolytics?
Test is used to diagnose CF
What is the sweat chloride test?
This condition causes coughing up of blood in older CF patients.
What is hemoptysis?
This CF-related metabolic disease affects blood sugar
What is cystic fibrosis-related diabetes?
Salty sweat poses this risk to the body
What is dehydration and electrolyte imbalance?
This therapy involves percussion and postural drainage
What is chest physiotherapy?
Nasal issue that is common in CF and leads to snoring
What are nasal polyps?
This is a long-term lung complication that can lead to heart failure.
What is pulmonary hypertension?
This happens if pancreatic enzymes are mixed with pudding or yogurt
What is the inactivation of the enzymes due to alkaline food?
CF patients often need supplements for which fat-soluble vitamins due to malabsorption issues
What are vitamins D, E, A, and K?
This is the best time to perform Chest PT
What is 1–2 hours after meals?