Medical management
When the chloride level in the sweat ranges between 60-200mEq/l
What is positive sweat chloride analysis
The underlying problem for CF which causes the formation of mucus that has little water content and is thick.
What is blocked chloride transport.
Focuses on weight maintenance, vitamin supplementation, DM management, and pancreatic enzyme replacement.
What is nutritional management
Performed to determine which specific mutation an adult may have. Different mutations result in different degrees of disease severity.
What is genetic testing
The thicky sticky mucus causes problems to these organs.
What is the lungs, pancreas, liver, salivary glands, and testes.
Use of positive expiatory pressure, active cycle breathing technique, and an individualized exercise program
What is preventative/maintenance therapy
Abdominal distention, gastroesophageal reflux, rectal prolapse, foul-smelling stools and steatorrhea.
What is nonpulmonary symptoms
Nonpulmonary problems included with a CF diagnosis
What is pancreatic insufficiency, malnutrition, intestinal obstruction, poor growth, male sterility and cirrhosis of the liver.
What is impaired gas exchange
ADEK
What are vitamin deficiencies common in patients with CF
What is osteoporosis, and diabetes mellitus
Increasing Paco2 and decreasing Pao2 are signs of respiratory failure. Severe hypoxemia and hypercarbia can lead to hypotension, dysrhythmias, and failing respiratory effort.
What is Monitor arterial blood gasses and oxygen saturation as indicated
need when the patient has increased chest congestion, reduced activity tolerance, increased or new onset crackles and a 10% decrease in FEV.
What is exacerbation therapy
The constant presence of thickened mucus interferes with Gas Exchange and results in this.
What is chronic respiratory tract infections, chronic bronchitis, and dilation of the bronchioles.
Supplemental oxygen maintains adequate oxygenation, decreases the work of breathing and calorie expenditure, and relieves dyspnea, increasing the level of comfort. Maintaining an oxygen saturation greater than 90% is the goal.
What is Administer oxygen therapy as indicated. (Avoid giving high oxygen concentration in clients with chronic carbon dioxide retention).