Etiology/Facts
Pathophysiology
Clinical Manifestations
Medical Management
Nursing Interventions
100
The type of trait that CF is
What is autosomal recessive?
100
The primary factor responsible for the clinical manifestations of CF
What is mechanical obstruction related to increased viscosity of mucous gland secretions?
100
The most prominent and consistent manifestation of pulmonary involvement in CF
What is chronic cough?
100
This helps loosen thick mucous and promotes airway clearance
What is chest physiotherapy?
100
The elements of a nursing respiratory assessment of a patient with CF
What are auscultation of lung sounds, observation of cough, and respiratory effort?
200
The incidence of having a child with CF if both parents carry the CF gene
What is 1 in 4 births?
200
Obstruction in the bronchioles due to thick mucous production leads to this
What is reduced gas exchange?
200
Hyperaeration of alveoli in CF leads to this
What is barrel-shaped chest?
200
These medications open bronchi to promote expectoration and lessen wheezing
What are bronchodilators?
200
The elements of a nursing gastrointestinal assessment of a patient with CF
What are frequency/characteristics of stool, monitoring for growth failure, adherence to enzyme regimen, and dietary intake?
300
The most common gene mutation found in CF
What is the delta-F508 gene?
300
Effect CF-related pancreatic duct blockage has on the body
What is unable to release pancreatic enzymes?
300
Unabsorbed fats excreted in the feces causes this
What is steatorrhea?
300
Patients with CF are often hospitalized for a chunk of time for this medical treatment
What is IV antibiotic administration?
300
A step nurses can take to assist patients and their families with coping
What is referral to community resources (counseling, clinics, online support groups, etc.)
400
The percentage of the CF population that is over 18 years old
What is almost 50%?
400
A decrease in the number of islets of Langerhans can lead to this
What is cystic fibrosis-related diabetes (CFRD)?
400
Decreased fat absorption can lead to these deficiencies
What are fat-soluble vitamin (A, D, E, K) deficiencies?
400
Severe pulmonary dysfunction may be an indication for this
What is a lung transplantation?
400
What a nurse can do to promote rest for a patient with CF?
What is cluster care and provide adequate pain management?
500
How CF is most commonly diagnosed
What is a sweat chloride test?
500
Percentage of males with CF that are sterile
What is more than 95%?
500
Excessive loss of sodium through sweat can lead to this
What is hyponatremia?
500
These medications aid in the digestion and absorption of nutrients
What are pancreatic enzymes?
500
Nursing strategies to prevent infection in patients with CF?
What are hand-hygiene, contact precautions, private rooms, and patient/family family education?
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