Hydrocephalus
Spina Bifida
Cleft Lip/Cleft Palate
Hip Dysplasia
Down Syndrome
100

What is Hydrocephalus?

Too much cerebrospinal fluid (CSF) within the ventricles of the brain which causes pressure changes in the brain and an increase in head size.

100

What is spina bifida?

Neural tube defect in which there is imperfect closure of the spinal vertebrae

100

After surgical repair of the cleft lip, what should the nurse do to prevent damage to the repaired lip?

Place elbow restraints on the infant.

100

What is hip dysplasia?

Head of the femur is partly or completely displaced as a result of a shallow hip socket

100

What causes trisomy 21?

Extra chromosome --> 3 chromosome 21s
200

True or False: Suspected hydrocephalus needs to be reported to the HCP promptly because delay in treatment can cause permanent brain damage.

True.

200

What prenatal supplement is recommended to prevent neural tube defects?

Folic acid supplementation during the early weeks of pregnancy. 400 mcg per day!

200

True or False: Infant cannot suck before or after surgery.

True. You wouldn’t want to apply tension to the sutures after surgery.

200

True or False: Treatment should be started as early as possible before ossification

True

200

How common is Down Syndrome?

1 in 700 live births

300

What is the classic sign of hydrocephalus?

An increase in head size (Bulging fontanelles)

*Nurses monitor for hydrocephalus by assessing fontanelles and head circumference.

300

Many infants with spina bifida develop a latex allergy. They should be taught to avoid foods associated with latex allergies. What are these foods? (3).

Bananas, avocados, kiwi

300

What do you use to feed an infant with cleft lip?

A syringe with rubber tip, a long nipple with a large hole attached to a squeeze bottle or a medicine dropper can be used to feed the infant.

300

What is one of the most reliable sign of hip dysplasia?

Limited abduction of the leg on the affected side

300

What type of defects are highly associated with down syndrome?

Congenital heart defects

400

How does a ventriculoperitoneal shunt (SHUNT) treat Hydrocephalus?

The shunt allows excess CSF to drain into the peritoneal cavity where it is absorbed.

400

How do you need to position an infant when they have been born with meningocele?

Place prone with a pad between the legs to maintain abduction.

 Can place the infant on their side to allow a break from the prone position.

400

What would you do post-operatively when caring for an infant who received post-operative care? (3)

Prevent sucking/crying to prevent damage to sutures

Apply elbow restraints

Position infant

400

Name 2 different treatment methods hip dysplasia.

Which is first line of treatment?

Pavlik Harness- First line of treatment

Spica Cast- used if the condition is caught late or not resolving with the Pavlik harness

400

What puts infants at risk for having down syndrome?

Advanced maternal age (>35 years old)

500

Name 4/6 signs of increased cranial pressure (ICP) in infants.

High-pitched cry, unequal pupil sizes, bulging fontanelles, irritability or lethargy, poor feeding, abnormal vital signs (low HR).

500

What should the nurse do with the sac when a baby is born with a meningocele?

Cover the sac with moist, sterile dressings
500

What is the patient with a cleft palate at risk for?

Increased risk of infections in the respiratory tract and middle ear.

*If not caught early, may cause deafness.

500

What type of assessments are important in those with spica casts?

Neurovascula

500

Name 3/5 manifestations of down syndrome.

vClose-set and upward-slanting eyes

Small head/round face

Flat nose and protruding tongue which affects sucking

Intellectual impairments

Congenital heart defects are HIGHLY ASSOCIATED WITH DS

600
How should you handle an infant's head who has hydrocephalus and why?


How do you position the infant after feeding and why?

*Support the head!

They already can’t support their head because of its size, with hydrocephalus it is larger and even harder to control.

*After feeding, an infant should be kept in a side lying position because vomiting occurs easily (risk for aspiration).

600

Name 3 interventions when caring for an infant with spina bifida

Prevent infection of injury to the sac

Correct positioning for sac protection and to prevent contractures

Keeping the infant clean and dry

Educating and supporting the parents

Ensuring adequate nutrition

600

Cleft palate: What is done after feedings to prevent speech problems and issues with the child's teeth?

The mouth is rinsed with sterile water.

600

Name 3 nursing interventions for a child with hip dysplasia.

Nursery nurse or post-partum nurse observes the newborn closely to see if there are signs of hip dysplasia and reports them.

Teach parents about the Pavlik harness and how to care for their baby in the harness

Neurovascular assessments in those with spica casts

 

Keeping the cast clean and dry, assisting with feeding, position changes and eliminating waste

Never shove anything down into a cast to itch the skin, you risk injuring the skin and getting an infection.

600

Who is your favorite teacher?

Mrs. Lewellen!

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