Hemophilia
What are some clinical manifestations of hemophilia?
Excessive bleeding, hematomas, joint pain
What is the shape of a sickle cell
"C" shape
What are the three types of anemia?
hyperproliferative
bleeding
hemolytic
ITP is what type of disorder?
autoimmune
What kind of blood disorder is thalassemia?
Inherited hemolytic anemia (genetic disorder)
Where is bleeding most likely to occur in patients with hemophilia?
The joints- knees, elbows, ankles, shoulders, wrists and hips
What is the most common symptom of a sickle cell crisis ?
Pain
What are risk factors of anemia?
rapid metabolic activity, diet, age
In this bleeding disorder what is decreased to cause the bleeding
platelets
What supplements are contraindicated with thalassemia?
iron supplements
what component of the blood is missing in hemophilia that causes bleeding?
Factor VIII and/or factor IX
How is sickle cell diagnosed?
Blood test, genetic testing
What lab values would be low with anemia?
Decrease iron, vit B12, folate, erythropoietin, RBC, H&H
ITP can result in a sever hemorrhage following what event(s)?
laceration / cesarean birth
What are the main manifestations of thalassemia?
anemia, bone deformities, jaundice, enlarged spleen, problems with liver growth, weakness and fatigue
What nursing education should be provided to parents of children with hemophilia?
Administration techniques of factor VIII and/or IX Prophylactically 3-4 times a week
avoid heat during bleeding episodes, wear medical alert bracelet, avoid roughhousing or contact sports.
What triggers a sickle cell crisis? (what should be avoided?)
What is an example of inherited hemolytic anemia?
Sickle cell
This procedure will be preformed if the body does not respond to medical management.
splenectomy
Which finding is most concerning for a patient with beta-thalassemia?
Iron overload (joint pain, weakness, liver dysfunction, cardiac dysfunctions
What sever complications can result from recumbent factor therapy?
Development of neutralizing antibodies to factor concentrates
What are treatment option for sickle cell crisis?
Pain management, RBC transfusion, hematopoietic stem cell transplant (HSCT)
What complications can anemia lead to?
heart failure, confusion, injury f/t falls
What is one of the medication used to treat ITP that can cause side effects and list the side effects of this medication?
Corticosteroids SE: infection, increased BS, osteoporosis
What is the rationale behind chelation therapy
to remove excess iron caused by frequent blood transfusions.