ALL
Hypoplastic Left Heart Syndrome
Croup
Sickle Cell Disease
Cystic Fibrosis
100

Which foods would a child with leukemia avoid?

- Mac & Cheese

- Baked Sweet Potatoes

- Roast Chicken

- Medium Rare Steak

What is medium rare steak?

100

This type of CHD is classified as a mixed defect in which the aorta is undersized and the left ventricle is either absent or underdeveloped.

What is Hypoplastic Left Heart Syndrome?

100

Croup is caused by _______.

What is swelling/inflammation in the upper airway due to an infection?

100

Name the abnormal type of hemoglobin that gives sickle cells their shape.

What is Hemoglobin S?

100

True/False: CF is an inherited respiratory disorder.

What is true?

200

What factors are most important for determining the prognosis of a child with ALL?

- Gender & Race

- Treatment choice and location of hospital

- Age @ diagnosis and initial WBC count

- Hct and Hgb levels

What are age @ diagnosis and initial WBC count.

200

HLHS is considered incompatible with life if there is no formation of an atrial septal defect, there is no patent foramen ovale or this opening between the aorta and pulmonary artery is closed.

What is the patent ductus arteriosus?

200

Signs & Symptoms of croup include _____.

(Must name 4 to get the points)

What are:

- Loud, bark-like cough

- Anxiety

- Fever

- Hoarse voice

- Labored breathing

- Runny nose/congestion

200

Name the definitive diagnostic test for SCD.

What is Hemoglobin Electrophoresis?

200

Which organ(s) is(are) affected by CF?

- Lungs

- Liver

- Pancreas

- All of the above

What is all of the above?

300

A new graduate RN has started her residency on the Onco floor.  Which of the following statements demonstrates her understanding of ALL?

- Patients with ALL have so many WBCs, they must be great at fighting infection.

- Lymphoblasts are immature WBCs that can't provide the immune support needed by the body.

- There is an overproduction of all cells in ALL, so patients rarely have issues with anemia.

- Surgery is the primary treatment for ALL.

What is lymphoblasts are immature WBCs that can't provide the immune support needed by the body?

300

In HLHS, this synthetic medication is vital for life and preserving oxygenation of the blood.

What are prostiglandins?

300

Pharmacological treatments include these two main drugs.

What are corticosteroid (Dexamethasone)

300

Name the most common cause of hospitalization in children with SCD.

What is vaso-occlusive crisis?

300

Which of the following are symptoms of CF? Select all that apply.

- Salty-tasting skin

- Frequent growth spurts

- Frequent lung infections

- Poor weight gain

- Heart palpitations

What are:

- Salty-tasting skin

- Frequent lung infections

- Poor weight gain

400

Which diagnostic procedures are appropriate for ALL? Select all that apply.

- LP

- CBC

- Bone Marrow Aspirate

- Ultrasound

- Brain MRI

What is LP, CBC, and Bone Marrow Aspirate?

400

Beyond the option for cardiac transplantation, looking specifically at palliative care for a patient with HLHS, there are this many procedures occurring in the first 2-3 years of life.

What is three?

400

Techniques to comfort and console a child with croup include _____.

(Must list at least 4 to get the points)

What are:

- Keeping the child calm to decrease coughing/crying.

- Distraction with favorite activities like singing, toys, or holding them.

- Humidified cool air.

- Sitting upright.

- Hydration.

- Rest

400
What kind of environment causes RBCs to sickle in someone who has SCD?

What is a low-oxygen environment?

400

A nurse is providing discharge teaching for a child who has CF.  Which of the following instructions should the nurse include?

- Provide low-calorie, low-protein diet

- Administer pancreatic enzyme capsules with meals and snacks

- Implement a fluid restriction during times of infection

- Restrict physical activity

What is administer pancreatic enzymes capsules with meals and snacks?

500

Which gland serves as a common site for lymphoblast accumulation?

- Thymus

- Pituitary

- Adrenal

- Thyroid

What is the thymus?

500

By the 2nd or 3rd year of life for a patient with HLHS, this final procedure connects the inferior vena cava and superior vena cava to the pulmonary artery allowing venous blood to shunt directly into the lungs without going through the ventricle.

What is the Fontan Procedure?

500

Croup generally lasts _____ and symptoms are worse _____.

What is 3-5 days AND at night?

500

Name a possible complication of SCD that should be managed prophylactically.

What is infection?

500

A nurse is admitting a child with CF.  Which of the following medications should the nurse anticipate administering? 

(Must get all for the points)

- Albuterol

- Oral glycemic medications

- Fat-soluble vitamins

- Water-soluble vitamins

- Gentamicin


What are:

- Albuterol

- Fat-Soluble Vitamins

- Gentamicin

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