Heterotaxy
Grab Bag
"I Used To Know That"
Who's your Reader?
Jewel or Junk
Measurements
Measurements
100
What is the definition of Hetero & -taxy?
The beginning of the word (hetero-) means “different” and the end (–taxy) means “arrangement.”
100
Why a VSD may not be heard on newborn screenings.
What are equal ventricular pressures
100
LVIDd is 5.0cm, LVIDs is 3.0cm
Fractional Shortening is ____% ?
LVIDd - LVIDs / LVIDd
5.0-3.0 / 5.0
Answer 40%
100
"Here's an Espresso Machine, I'm headed to Chicago"
Who is Dr. Matt Moehlmann
100
Measuring TR Peak in HLHS RV
Junk RVP is Systemic, B/P
200
What are the two (2) types of Heterotaxy
Right Isomerism or Right Atrial Isomerism
&
Left Isomerism or Left Atrial Isomerism
200
What type of interruption?
Type A
200
This syndrome is associated with IAA type B, aortic arch anomalies, truncus arteriosus & TOF
What is Di George or 22q11.2 deletion syndrome
200
Can you get me 3D on this patient???
Who is Maria Kiaffas.
200
How accurate is PV gradient in setting of VSD
Junk, additional volume from VSD adding to PV gradient
300
"Asplenia" is associated with which type of Heterotaxy
Right Atrial Isomerism
300
Which image is a DORV and why?
Subaortic conus, 1st image
300
The Truncal Valve in Truncus Arteriosus is most commonly:
A. Unicuspid
B Bicuspid
C. Tricuspid
D. Quadricuspid
C. Tricuspid 42%
Bi 30%, Quad 24%, Uni 1%
300
Who is Nitin Madan
300
Why do you need to be careful in interpreting this Doppler image?
There is multilevel obstruction-dynamic, infundibular, and total maximal gradient.
400
Which of the following is not usually associated with Left or Left Atrial Isomerism
A. Interupted IVC
B. TAPVR
C. Heart Block
B. TAPVR is usually associated with Right or
Right Atrial Isomerism
400
Ratio of Noncompacted to compacted Myocardium to be diagnosed with LV NonCompaction:
A. > or = to 1.9
B. > or = to 2.3
C. > or = to 2.7
D. > or = to 3.1
The Baseline ratio to diagnosis of LVNC is.
B. Greater than or equal to ratio of 2.3 Noncompacted myocardium to compacted myocardium.
400
What are normal oxygen saturations for single ventricle circulation?
75%-85%
400
Who is Sanket Shah
400
AS gradient in heart with diminished LV function
Junk, poor squeeze masks true obstruction
500
Which type of Heterotaxy is associated with LV NonCompaction and Why?
Left Isomerism
Because of heart block
500
Main contributor to Contraindication of Norwood Procedure on HLHS with Turner's syndrome.
What is Lymphatic System Abnormalities
500
Cardiac Lesion where
1. Great Arteries arise in parallel fashion from the correct Ventricles
2. Aorta is anterior to the PA
3. There is no Aortic Mitral continuity
What is Anatomically Corrected Malposition of the Great Arteries
500
Who is:
ASM Connect Message:
"I've got numbers and report. Go to the next echo".
Who is Dan Forsha
500
Post ASO
Coronary Doppler
Jewel
Doppler gradient <1.6m/sec correlates with patency of ostia post re-implantation