Sickle Cell Anemia
Sickle Cell Crisis
Hemophilia
Anemia
Grab Bag
100
In SCA this is replaced by an abnormal cell.
What is hemoglobin
100
This activity level should be ordered for a child in SSC.
What is Bedrest?
100
80% of those with hemophilia have a deficiency of this
What is Factor VIII?
100
What two malabsorption disorders can lead to iron deficiency anemia?
What are lactose intolerance and inflammatory bowel disease?
100
A mother of Japanese decent states that she keeps her daughter's 30 day supply of iron pills on top of the refrigerator. What education might she need?
What is tea decreases the absorption of iron.
200
The majority of deaths in children with SCA are caused by this complication
What is infection
200
What is the skeletal problem that frequently occurs in children ages 6 months to 2 years in a vaso-occlusive crisis?
What is dactylitis (hand-and-foot syndrome)?
200
Those with hemophilia should wear one of these.
What is a medical alert bracelet?
200
Elevation of this is the body's compensatory mechanism to absorb more iron from exogenous sources?
What is Total Iron-binding capacity (TIBC)?
200
Name 2 high folate foods
What are fortified cereals, lentils, spinach, broccoli, northern beans, asparagus, cantaloupe, and eggs
300
Obstruction caused by sickled RBCs, vascular inflammation, and what other manifestation are the primary results of SCA?
What is RBC destruction
300
When teaching parents, what might you suggest to provide comfort to affected areas?
What is heat application?
300
Those with hemophilia should avoid what medications?
What are aspirin and NSAIDs?
300
The primary way nurses can prevent nutritional anemia is through this.
What is family education?
300
You are educating a mother on when to administer iron supplements to her child. What time and with what liquid is best?
What is 2 divided doses between meals with citrus or juice?
400
A patient with SCA begins to slur their words. What complication are you most concerned they are experiencing?
What is stroke?
400
What is the most common trigger for a crisis?
What is dehydration (inability to concentrate urine)?
400
The administration of this medication should result in a 3-4 fold increase in Factor VIII.
What is vasopressin or DDVAP?
400
Universal screening for anemia is done at what age?
What is 12 months old?
400
The guardian of a 2 month old girl just diagnosed with SCA has asked "How do I know when to bring her back into the doctor?" What would your response be?
What is he/she should seek medical attention for fever>101.3F, pallor, splenomegaly, and increasing pain
500
This is the only drug approved to decrease painful episodes and ACS.
What is Hydroxyurea?
500
Repeated episodes of ACS can result in these two sequelae.
What is restrictive lung disease and pulmonary hypertension?
500
Adjunct therapy for hemathrosis includes these interventions.
What are rest, ice, elevation, splint, ACE wrap, and physical therapy?
500
Your 11 year old female patient's vital signs are as follows: HR 118 RR 26 BP 88/52 O2 98% T 36.2C Which VS is most concerning for anemia?
What is her blood pressure?
500
An infant had profuse bleeding after a circumcision, after stopping the bleeding and replacing the volume with pRBCs you would encourage the team to refer the family to what professional?
What is a genetic counselor?
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