These Genes Fit
Rheum for More
Name that Tune
Rhythm and Blues
Potpourri
100
Valvular pulmonary stenosis. Seen most commonly in which syndrome
What is Noonan syndrome
100
Delayed, non-suppurative sequela of infection with group A beta-hemolytic streptococci or Streptococcus pyogenes. The acute phase of ARF (acute rheumatic fever) is caused by a proliferative inflammatory reaction that involves the connective and/or collagen tissues and can affects multi-organ systems. Name the major criteria for ARF
What is JONES criteria: Joint involvement, Heart involvement (pericarditis, pericardial effusion), Nodules, Erythema marginatum, Sydenham's Chorea. Minor criteria: High CRP/ESR, fever, arthralgia, and prolonged PR interval.
100
Left lower sternal border. Vibratory, louder when supine.
What is Still's murmur
100
Pre-excited depolarization of QRS complex (delta waves). Seen in what syndrome
What is Wolff-Parkinson-White syndrome
100
Most common cause of myocarditis
What is viral (Enterovirus, Parvovirus, Adenovirus etc.)
200
Cardiac rhabdomyomas. Seen most commonly in which syndrome
What is Tuberous Sclerosis
200
CC: High fever for 6 days. PI: Six days prior to admission (PTA), she developed high fever and rhinorrhea. She was taken to see a doctor at a clinic and was diagnosed with "URI". She was prescribed Tylenonl, amoxicillin. Two days PTA, she had semi-solid stool. One day PTA, she developed maculopapular rash at trunk at extremities. PH: she had been healthy. Birth weight was 2.8 kgs. Significant PE An infant, fully conscious but irritable, body weigh 5.2 kgs. Vital signs: Temp 39.8 C, HR 160 beats/min, RR 40 breaths/min, BP 98/50 mmHg HEENT: mild injected conjunctiva, no icteric sclera, red lips. Lymph node: not palpable Heart: regular rhythm, tachycardia Lung: clear, no adventitious sound Abdomen: soft, no organomegaly Skin : Erythematous rash at trunk and extremities Extremities: Swelling of dorsal part of hands and feet Disease at top of differential
What is Kawasaki Disease
200
Left upper sternal border. Loudest in axillae. Systolic and seen in infants.
What is Peripheral Pulmonic Stenosis (PPS)
200
Tet spells, boot-shaped heart, single second heart sound -- all can be seen in Tetralogy of Fallot. Name the 4 heart defects.
What is VSD, pulmonary stenosis, overriding aorta, right ventricular hypertrophy
200
4 day old with cyanosis, cool extremities, lethargy. What's on your differential (any 3 for credit)
What is left heart obstructive lesions: aortic stenosis, coarcation of aorta, hypoplastic left heart syndrome
300
Supravalvular aortic stenosis. Seen most commonly in which syndrome
What is Williams syndrome
300
Which heart valve is most commonly affected by ARF
What is mitral valve
300
Right upper sternal border. Continuous, disappears with jugular vein compression or when head turned or upon being supine.
What is venous hum
300
During a "tet spell," what is immediate therapy (Name 3/4 get credit)
What is knee-to-chest position, sodium bicarbonate, morphine, and oxygen. Surgery is not an immediate treatment!
300
Newborns with hypoplastic left heart syndrome, pulmonary atresia, interrupted aortic arch, & critical pulmonary stenosis may all need this medication after birth.
What is prostaglandin (PGE)
400
Dissection of the ascending aorta. Seen most commonly in which syndrome
What is Marfan syndrome
400
The most common arrhythmia leading to fetal bradycardia
What is complete heart block (SS-A/Ro or SS-B/la)
400
Left upper sternal border. Systolic, fixed split S2
What is ASD
400
A one year old presents to the clinic in SVT. What is the most common method used to try and convert out of SVT in this scenario
What is bag of ice on the face
400
Which meds are associated with drug induced long QT syndrome?
What is amitriptyline, azithromycin/erythromycin, cisapride (removed from market)
500
Endocardial cushion defect. Seen most commonly in which syndrome
What is Down syndrome
500
Diagnostic criteria for Kawasaki? Need full answer for credit.
What is fever >5 days plus: Conjunctival injection (non-exudative) Rash (polymorphous, non-vesicular, mostly truncal) Adenopathy (cervical) Strawberry tongue (changes of the mucosa of the oropharynx, including an injected pharynx, an injected and/or dry fissured lips, and a strawberry tongue) Hands/feet edema
500
Left lower sternal border. Holosystolic/pansystolic, harsh
What is VSD
500
Progressive prolongation of the PR interval on the ECG on consecutive beats followed by a blocked P wave (i.e., a "dropped" QRS complex). After the dropped QRS complex, the PR interval resets and the cycle repeats
What is second degree AV block, Mobitz type I (Wenckebach)
500
It was the first successful surgical procedure for congenital heart disease performed in 1938 by Dr. Robert E. Gross at Children's Hospital Boston
What is PDA ligation
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