More on Clefts
The name for the translucent bluish covering of a submucous cleft
What is the zona pellucida?
The device to repair a cleft palate that is fitted at one week, has weekly fittings and adjustments, has a nasal bulb attached at 5mm, is closed at 1mm and PE tubes are inserted
What is nasoalveolar ridge molding (NAM)?
The inadequate closure of the velopharyngeal port due to a structural deficiency
What is velopharyngeal insufficiency?
The type of airflow for sucking, blowing, singing, and speech with a low velum in the pharynx and outward bowed LPWs
What is pneumatic?
The name of 1 syndrome we learned about in class (other than your own)
What are Angelman, Williams, Cornelia de Lange, 22q11.2, Fragile X, Kabuki, Familial Dysautonomia, Wolf Hirshhorn, Cri du Chat, Moebius, Prader-Willi
There are no feeding problems if there is correct nipple place
There are no hearing, resonance, or speech problems
The type of cleft that this summary belongs to
What is an incomplete cleft lip?
The 2 major stages of surgical management
What are primary and secondary corrections?
The inadequate closure of the velopharyngeal port due to a functional deficiency
What is velopharyngeal incompetency?
The two types of intervention for VP Insufficiency that were discussed in class
What are CPAP and PiNCH?
The most significant key clinical feature of Angelman Syndrome
The type of cleft that has difficulty forming a seal and the oral pressure necessary for sucking, experiences nasal regurgitation, needing adaptive positioning, has no hearing deficits, is hypernasal, and has difficulties with nasal air emissions and overall articulation
What is a complete cleft lip?
The two main/general lip surgeries
What are Millard and Randall-Tennison (RT)?
The type of nasal air emission that occurs when producing nasal sounds
What is audible NAE?
The type of intervention that would only be considered if a person with VPI associated with cleft palate cannot undergo surgery
What is a speech bulb?
The most severe and life threatening comorbidity in Williams Syndrome
What is cardiovascular disease?
The 3 causes of a cleft lip and palate
What are endogenous, exogenous, and multifactorial?
The primary surgery types for cleft palate closure
The types of adjectives that can be used to describe a voice (name 4 for full points)
What are hoarse, breathy, strained, tense, harsh, scratchy, deep, high pitched, squeaky, shaky, gravelly, effortful, raspy
The 4 types of resonance disorders discussed in class
What are hypernasality, nasal air emission, hyponasality and denasality, and cul-de-sac resonance
The syndrome where individuals with it have excessive hair that contributes to convergent eyebrows and long eyelashes
What is Cornelia de Lange Syndrome?
The signs of a submucous cleft (list 3 to get full points)
What are a bifid uvula, zona pellucida, hypernasality, nasal air emissions, nasal regurgitation, chronic otitis media
The surgical aims for cleft lip and palate (name 3 to receive full points)
The five main reasons for VPI
What are insufficient tissue, a neurological or muscular disorder, a deep pharynx, a mechanical obstruction, and producing a hypernasal voice deliberately or through habit?
The five secondary surgical interventions
What are implantation, velar pushback, superior based pharyngeal flap, sphincter pharyngoplasty (bilateral flaps), and double z furlow
The syndrome that is incredibly rare and congenital that with an occurrence of 1:250,000 births
What is Moebius Syndrome?