Anatomy and Physiology
Pulmonary Function Tests
Organs
Disease
Treatments
100
Medical complications associated with cystic fibrosis primarily involve these two organ systems.
What are the respiratory and the gastrointestinal systems?
100
This test measures how much air can be exhaled after a patient takes his/her deepest breath, and blows out as forcefully as possible.
What is Spirometry?
100
Greater than 95% of males have disfunction in this organ system.
What is the reproductive system?
100
CF is known to be the most common fatal genetic disease in this ethnic group.
What are Caucasians?
100
This category of treatment is used to eradicate bacterial infections in the lungs
What are antibiotics?
200
The estimated number of people in the U.S. affected by CF.
What is 30,000
200
This test is the most commonly used marker for airway disease and is highly correlated with mortality in CF.
What is FEV1?
200
This is considered to be both an exocrine gland as well as an endocrine gland.
What is the pancreas?
200
This is the current median age of survival for people with CF in the U.S.
What is 37.4 years of age?
200
This category of treatment is used to reduce airway inflammation.
What are anti-inflammatories?
300
Cystic fibrosis is caused by the mutation of a gene on this chromosome.
What is chromosome 7
300
This is the total amount of air a patient's lungs can hold.
What is Total Lung Capacity or TLC?
300
This organ's role in digestion is through the production of bile.
What is the liver?
300
More than 70 percent of people with CF are diagnosed by this age.
What is 2 years of age?
300
This category of treatment is used as a nasal spray for short term relief from sinusitis and nasal polyps.
What are antihistamines?
400
This protein functions as a chloride channel across membranes of cells that produce mucus, sweat, saliva, tears, and digestive enzymes.
What is CFTR?
400
This is the FEV1 score associated with severe lung disease.
What is an FEV1 of <40%?
400
This organ system consists of the nose, pharynx and sinuses.
What is the upper respiratory system?
400
This is the most common inital diagnostic test for CF, due to it's sensitivity and low cost.
What is the sweat test?
400
These are the three ways that antibiotic therapy can be administered.
What is: -orally -intravenously (IV) -inhaled
500
Members of the CF community prefer to be referred to by this terminology.
What is "people living with CF"
500
This is the FEV1 score that is associated with Normal lung function.
What is an FEV1 score of >_ to 90%?
500
The effects on this organ system are associted with pale or clay colored stool and weight loss.
What is the gastrointestinal or GI system?
500
These are the 3 of the 5 hallmark features of CF.
What are: -chronic pulmonary infection -bronchiectasis -exocrine pancreatic insufficiency -elevated sweat chloride -male infertility
500
According to the CFF Medication Guidelines, these two medications that are "Strongly" recommended.
What are TOBI and Pulmozyme?