name the problem
recurrent severe infections
opportunistic infections
FTT
persistent thrush
chronic diarrhea
what are signs of an immunodeficient child (esp T cell defect)
five years
at what age can spirometry be performed
what drugs are used for eosinophilic asthma
bonus: how do we diagnose that?
eczema, thrombocytopenia, recurrent infection
what is wiskott aldrich sydrome?
bonus: how do we treat
Complement total
what test would you send to screen for recurrent Neisseria infection or sepsis
bonus: how would you treat this child
XLA
selective IGA deficiency
CVID
asthma action plan
what should all patients receive upon discharge with asthma
Berinert, Firazyr, orladeo
what are drugs used to treat HAE
bonus: what is available for prophylaxis
asthma, eosinophilia, neuropathy
what is EGPA
a child with recurrent giardia infections
what is selective IGA deficiency
SCID
DIgeorge Syndrome
Hyper IGM syndrome
what are some combined immune deficiencies
exercise, URI, allergens
what are triggers of asthma
live viral vaccines
eczema, recurrent skin abscesses, pneumonia, retained primary teeth
what are signs of Hyper IGE
bonus: what is the genetic defect?
chronic lymphadenopathy and autoimmune cytopenia
how do patients with ALPS present
CGD
LAD
what are phagocytic disorders
bonus how do we treat them?
spirometry and FENO
what are tests utilized to help guage compliance with asthma treatment
PEG ADA
what medications are used to treat ADA SCID
bonus: name another therapy
delayed umbilical cord separation, gingivitis
what is leukocyte adhesion deficiency
bonus: how do we treat this child?
internal medicine or pediatric residency
what is a pre-requisite for an allergy fellowhip
fever > 5 days
conjunctivitis
oral mucosa changes
rash
coronary artery aneurism
what are signs of Kawasaki disease
what is the treatment
anti IL-5, Anti IL4/13, anti IGE, anti TSLP
what biologics are used in asthma
cytoxan, nucala
what medications may be used to treat EGPA
low TREC
what test is used to screen for SCID by Newborn screening
bonus: what else can cause false positive
a 6 month old with recurrent otitis media, chronic diarrhea
what are signs of XLA
bonus: what do you measure, which genetic test.