What is the name of the famous baseball player who has struggled with ALS (Amyotrophic Lateral Sclerosis) and is also another name for this disease.
Who is Lou Gehrig
100
Tongue atrophy, weakness in arms and hands, fasciculation’s of the face, Dysphagia, and Dysarthria
What are early signs of ALS
100
Strengthen of uninvolved muscles and prevent disuse atrophy
What is perform active exercise, and range of motion exercise
100
Need nutrition consult
What is need for planning meals that the pt can not swallow
100
50 mg of this________ is given twice a day
What is Rilozule (Rilutek)
200
What is the overall, eventual outcome of ALS (Amyotrophic Lateral Sclerosis)
What is paralysis and death
200
Diagnostic studies should reveal motor strength deficits in what
What are muscle testing, pulmonary function, and dyspahigia
200
Prevent aspiration
What is instruct a patient to drink and eat in an upright position with neck flexed
200
Sufficient nutrients
What is family teaching to ensure that the pt. obtains sufficient, fiber, and fluids
200
Patient is at risk for what while taking Rilozule (Rilutek
What is liver toxicity
300
What are the only nerve cells that are affected by ALS (Amyotrophic Lateral Sclerosis) These nerve cells control movement of the limbs, swallowing, and some aspects of breathing
What are lower motor neurons
300
A ________ demonstrates small, angulated, atrophic fibers
What is a muscle biopsy
300
Keep patient mobile as long as possible
What is utilize braces, splints and canes
300
When the patient can no longer swallow
What is placement of feeding tube
300
For speech and swallowing difficulties you would consult
What is speech-language pathologist
400
What are some of the environmental things that may trigger ALS ( Amyotrophic Lateral Sclerosis)
What are heavy metals, animal hides, fertilizers, viral infection, severe physical trauma
400
Demonstrates fibrillations and fasciculation’s of the muscles
What is an electromyogram
400
Vision, ocular movement, intelegence, consciousness and alertness
What are things that an ALS patient retains even after paralysis
400
Based on pt decision or advance directive
What is dietician recommendation of enteral feeding
400
During end stage of the disease some patients will be placed on what
What is mechanical ventilation
500
What is the name of the enzyme that is prevented from being made by a defective gene in the disease ALS ( Amyotrophic Lateral Sclerosis)
What is Superoxide Dismutase
500
This lab value is increased
What is creatinine kinase
500
The most common cause of dealth in ALS patients
What is respiratory failure due to lung muscles paralysis
500
No food
What is pt teaching on diet related to drug Riluzole (Ritutek)
500
These are used for symptomatic dyspnea and/or intractable pain