Cystic Fribosis
Heredity
Nursing Knowledge and Expectations
Culture
100
During the genetic test, CFTR genes may show up signaling that the patient has CF. Are CFTR genes dominant or recessive?
What is recessive
100
What type of hereditary disorder is cystic fibrosis?
What is autosomal recessive
100
Where is Mark in his developmental stage according to Erickson, and Piaget theories of development?
What is Mark is in Erikson’s Industry & Inferiority stage
100
What is culture?
What is The thoughts, communication, actions, customs, beliefs, values, and institutions of racial, ethnic, religious, or social groups
200
Name two of the four symptoms of CF mentioned in the readings.
What is difficulty breathing, chronic lung infection, failure to grow or gain weight and difficulty digesting food.
200
Which protein is affected in cystic fibrosis?
What is CFTR protein
200
When should treatment take place?
When is before meals as coughing can stimulate vomiting
200
What is race?
What is a group of people who share biologic similarities such as skin color, bone structure, and genetic traits
300
Do medications such as antibiotics, bronchodilators and mucus thinning drugs help people with CF?
What is yes they do. These medications can help reduce the symptoms, but it won’t get rid of CF.
300
In the case where both parents are carriers what is the chance that the abnormal CF gene would be passed on to any of their offspring’s?
What is 25%
300
What does cystic fibrosis treatment focus on?
What is controlling infection and inflammation and reducing mucus accumulation
300
What is the most important characteristic of ethnic group
What is a sense of common identity
400
How many people in the Caucasian population have CF (in other words, one in how many people?)
What is 1 in 2500
400
What is pneumonia and its correlation with cystic fibrosis?
What is an inflammation of the bronchioles and alveolar spaces in the lungs. Children with cystic fibrosis or immunocompromised are susceptible to other bacterial, parasitic, or fungal infections.
400
To what age group can a pediatrician can have as their clients?
What are adolescents and teens? Pediatricians are specialized up to adolescences as their clients, as in they can still take teens as their patients, however many teens tend to start seeing a Family Doctor at this point so they won’t have to change over later, and they can be more comfortable with their doctors to be open and honest.
400
What is Cultural Competence?
What is the ability to understand and effectively respond to the needs of individuals and families from different backgrounds
500
True or False. The patient has high salt levels in their sweat during a sweat test, do they likely have CF?
What is yes
500
List 2 of 4 common diagnosis for a child with cystic fibrosis?
What is a) Ineffective Airway clearance realted to thick mucus in lungs b) Risk for infection related to the presence of mucous secretions conductive to bacterial growth c) Imbalanced Nutrition: less than body requireents related to need for increased calories to meet metabolic needs d) Parental Role Conflict related to interruptions in family life due to the home care regimen and child`s frequent exacerbations.
500
What medication is used following a bronchodilator? This solution potentially improves mucus clearance by increasing hydration of the airway
What is Hypertonic saline (7%)
500
What is cultural pluralism?
What is perspective, appreciating differences among varying culture groups, promoting respect for rights of others to have different values, beliefs, ways of life