inherited disorders: jaw bone & facies
disorder that can cause bilateral facial swelling, interrupt tooth development/eruption, and radiographically presented as "soap-bubble" in the ascending ramus & molar/premolar area (mandible) or tuberositiy (maxilla) ?
what is cherubism ?
developmental bony growths present on the hard palate and/or the lingual aspect of the mandible.
what is torus palatinus ? what is torus mandibularis?
gingival hypertrophy that generally develops early in life and may cause dense connective tissue that overgrow teeth.
what is gingival fibromatosis ?
patient clinically presents with a small face, prominent enlargement of (occipital, parietal, frontal bones), long/narrow neck, and hypoplasia of clavicles. These individuals present w/ supernumerary teeth.
what is cleidocranial dysplasia?
disorder characterized by a cyclic decrease in the number of circulation cyclic neutrophils.
what is cyclic neutropenia?
treatment of gingival fibromitosis
what is surgical removal of tissue? what is proper hygiene care to reduce the risk of secondary inflammation and infection in the deep pseudopockets?
autosomal dominant inheritance pattern. Disease presents with multiple osteomas, odontomas, and/or intestinal polyps that may become malignant at the age of 30 or above.
What is Gardener Syndrome?
the duration for cycle intervals and neutropenic episodes of cyclic neutropenia. Treatment when neutrophil count is normal.
what is the cyclic interval of 21-27 days? what is the neutropenia episode of 2-3 days? What is the best time to treat a patient with cyclic neutropenia?
oral manifestations of gingival fibromatosis
what is gingival hypertrophy that overgrows teeth, firm tissue w/ a granular corrugated surface, pale gingiva, and lip protrusion?
autosomal dominant inheritance pattern. Clinically presents w/ a hypoplastic nose, hypoplastic malar bones with hypoplasia or absence of zygomatic process. Patients may also have misplaced ears, receding chin, clefting of lower eyelids and/or deafness.
what is mandibulofacial dysplasia?
Disorder presenting with decreased neutrophils. Patients clinically present severe destruction of periodontal tissues, loss of both primary and permanent teeth, and red scaly keratosis of palms of hands and soles of feet.
what is Papillon Lefevre Syndrome ?
inheritance pattern is autosomal dominant. Disease clinically presents with increased distance between eyes - basal cell carcinomas over the (eyes, cheeks, neck, arms, etc.). Orally presents w/ multiple odontokeratocysts (may develop as early as 5 or 6 years old)
what is Nevoid Basal Cell Carcinoma Syndrome?
clinical radiopraph presentation AND treatment of Papillon Lefevre Syndrome.
what is the radiographic presentation of marked alveolar bone resorption with vertical pockets and tooth loss in the same sequence as they were erupted? What is no treatment for Papillion LeFevre Syndrome?