CF 101
Mary has CF and has fatty stools what’s the first thing the nurse will inquire about?
Has the patient been taking pancreatic enzymes
________________ is a respiratory condition that is considered a medical emergency. This disorder is one of the only time assessments can not be performed. As we dont want to startle the child. The patient may be drooling, tripoding, frog like sounds, muffled voice, and may require trace or ET
Epiglottis
Decreased pulmonary blood flow disease that has four disorders associated with it Pulmonary stenosis, VSD, Overriding aorta, and Right Ventricle hypertrophy.
Associated with Tet Spells
Tetralogy of Fallot
Inherited blood disorder where Malformed RBC bone pain and fractures commonly seen. Common in Mediterranean people. Complication include Spleen enlargement and over stimulation of bone marrow.
Poor Prognosis child dies from cardiac issues
Treatment blood transfusion to keep HGB above 10 and bm transplant
Thalassemia
Lakea has iron deficiency anemia. She is wondering what non pharmocological inteerventions she can do to help increase her iron.
Red meats, lentils, green leafy vegetables, peanut butter and died beans.
She can also take her iron supplements with orange juice as it aids in absorption.
Can Cystic Fibrosis patients can share rooms
No
Atrovent and Albuterol are considered what type of medication for asthma?
Short Acting Quick relief
________________________ is a Mixed blood disorder where armies are misplaced. You you keep the PDA and ASD open using ____________
Transposition of Great arteries and prostaglandin
Time frame for blood products
Blood 4h
Plasma 2hr
Platlet 1hr
Total time form bank to end of transfusion
This disease is marked by low HGB HIGH WBC High bilirubin misshaped rBC most common inherited blood disorder and primarily affect African Americans
Sickle Cell
What us treatment for CF Cystic Fibrosis
laxative & stool softener, high salt diet, albuterol, cholinergics, pancreatic enzymes, Insulin, Vitamins ADE&K chest physiotherapy
enzymes within 3o min of each meal
Priorities for a child with who had a tonsillectomy
Alert for bleeding, Upright position, Frequent swallowing
Suction equipment. 5th-7th day more at risk for hemorrhaging. No red drinks or acidic drinks.
___________________ is normally found in sports physicals and is characterized by narrowing of the lumen of the aorta usually at or near the PDA.
Bounding pulses in upper extremities and decreased BP
Coarctation of the aorta
_________________ is a type of sickle cell crisis than can be caused by a virus respiratory in nature and can be a medical emergency
Acute Chest
Pulse hard to locate, Faint pulses, hypotension, tachycardia, poor feeding, intolerance to excercise are symptoms mof what disorder
Aortic Stenosis
________________ vaccine prevents Epiglottis
HIB
Medications that can trigger asthma- reactive airway
Aspirin, Nsaids, and beta blockers
This disease is marked by pulse being hard to find and narrowing of the aortic valve. can be treated by ballon dilation beta blockers and CCB
Norwood and Valvotomy
Aortic Stenosis
Makala 16 years old entered the ED at she is having a sickle cell crisis she is in severe pain. She stated that she had take OTC pain meds at home and nothing seemed to help. She is being admitted at 1730. Alana is her nurse. What is the nursing interventions for MaKala in order that they are prioritized
HYDRATION- help to lessen the viscosity of the blood
Pain MED-IV PAIN MEDs by 1800. Pain med within 30 mins Oxygenation
_____________ is a type of sickle cell crisis where blood pools in the spleen the child can die within hours and is common in children under 2 years old
Spleinc Sequestration
___________________ is a respiratory disease that causes production of thick mucous that affects pancreas, liver, and reproductive organs. It mostly affects caucasians.
Cystic Fibrosisi
Tet Spell is consider a medical __________ how should you treat a TeT spell
EMERGENCY!!! Morphine Knee chest and oxygen
Vasopressin is used to treat what type of hemophilia
Hemophillia A
This bleeding disorder is characterized by low platelets usually around 100k labs for this disorder include PT, PTT INR Fibrinogen and D-Dimer
ITP
What are signs of respiratory distress
Tripoding, nasal flaring, grunting, Apnea, dyspnea, chest wall reces, head bobbing.