These Genes Fit
Rheum for More
Name that Tune
Rhythm & Blues
Mixed Beats
100

Valvular pulmonary stenosis. Seen most commonly in this syndrome

What is Noonan syndrome

100

This mnemonic outlines the major criteria used to diagnose acute rheumatic fever. 

What is the JONES criteria?

  • J – Joints (migratory polyarthritis)

  • O – ❤️ (Heart: carditis, including endo-, myo-, or pericarditis)

  • N – Nodules (subcutaneous)

  • E – Erythema marginatum

  • S – Sydenham’s chorea

100

Left lower sternal border murmur. Vibratory, louder when supine.

What is Still's murmur

100

Pre-excited depolarization of QRS complex (delta waves). Seen in this syndrome

What is Wolff-Parkinson-White syndrome

100

The most common cause of myocarditis in children.

What is viral infection?

 (Enterovirus, Parvovirus, Adenovirus etc.)

200

Cardiac rhabdomyomas. Seen most commonly in this syndrome

What is Tuberous Sclerosis

200

This vasculitis should top your differential in a febrile infant with conjunctival injection, red lips, rash, and swelling of hands and feet after six days of persistent high fever.

What is Kawasaki Disease

200

Left upper sternal border. Loudest in axillae. Systolic and seen in infants.

What is Peripheral Pulmonic Stenosis (PPS)

200
Tet spells, boot-shaped heart, single second heart sound -- all can be seen in Tetralogy of Fallot. Name the 4 heart defects.
What is VSD, pulmonary stenosis, overriding aorta, right ventricular hypertrophy
200

4 day old with cyanosis, cool extremities, lethargy. What's on your differential (any 3 for credit)

What is left heart obstructive lesions: aortic stenosis, coarcation of aorta, hypoplastic left heart syndrome

300

Supravalvular aortic stenosis. Seen most commonly in this syndrome

What is Williams syndrome

300

This heart valve is the most commonly affected by ARF

What is mitral valve

300

Right upper sternal border. Continuous, disappears with jugular vein compression or when head turned or upon being supine.

What is venous hum

300

During a "tet spell," this is the immediate therapy (Name 3/4 get credit)

What is knee-to-chest position, sodium bicarbonate, morphine, and oxygen. Surgery is not an immediate treatment!

300
Newborns with hypoplastic left heart syndrome, pulmonary atresia, interrupted aortic arch, & critical pulmonary stenosis may all need this medication after birth.
What is prostaglandin (PGE)
400

Dissection of the ascending aorta. Seen most commonly in this syndrome

What is Marfan syndrome

400

The most common arrhythmia leading to fetal bradycardia

What is complete heart block (SS-A/Ro or SS-B/la)

400
Left upper sternal border. Systolic, fixed split S2
What is ASD
400
A one year old presents to the clinic in SVT. What is the most common method used to try and convert out of SVT in this scenario
What is bag of ice on the face
400

Which meds are associated with drug induced long QT syndrome?

What is amitriptyline, azithromycin/erythromycin, cisapride (removed from market)

500

Endocardial cushion defect. Seen most commonly in this syndrome

What is Down syndrome

500

This cardiac complication, often subclinical, is associated with the systemic subtype of juvenile idiopathic arthritis and can present with muffled heart sounds, pulsus paradoxus, or even tamponade physiology.

What is pericarditis?

500
Left lower sternal border. Holosystolic/pansystolic, harsh
What is VSD
500

Progressive prolongation of the PR interval on the ECG on consecutive beats followed by a blocked P wave (i.e., a "dropped" QRS complex). After the dropped QRS complex, the PR interval resets and the cycle repeats

What is second degree AV block, Mobitz type I (Wenckebach)

500
It was the first successful surgical procedure for congenital heart disease performed in 1938 by Dr. Robert E. Gross at Children's Hospital Boston
What is PDA ligation