Sickle Cell Disease
Autism Spectrum Disorder
Langerhans Cell Histiocytosis
PHACES
Landau-Kleffner Syndrome
100

This inherited disease affects what?

What is red blood cells
100

Speech, language, auditory, and behavioral deficits may be seen due to this

What is sensory and auditory processing 

100

LCH is a disorder of abnormal production of what?

What is white blood cells

100

This is what type of syndrome?

What is congenital

100

This childhood epilepsy syndrome is also know to include?

What is progressive neuropsychological impairment

200

This disease often leads to children having what type and degree of hearing loss?

What is mild to profound Sensorineural HL.  Bonus +100What is sloping in the high frequencies

200

This is one area that ASD is not established to be caused by?

What is immunologic factors

200

This condition impacts what 3 structures of the body?

What is Skin, Bone, and Ear

200

What does each letter if the acronym stand for with this syndrome?

What is posterior fossa, hemangiomas, arterial anomalies, cardiac anomalies, eye anomalies, and sternal cleating

200

This syndrome is most common in what population?

What is males between 4-7

300

These treatments for SCD can be ototoxic

What is blood transfusion and iron chelation therapy 

300
This is basis of the newest theory for ASD

What is neurobiology changes in the brain

Bonus +100 abnormalities in dendritic spines

300

What type and lateralization of hearing loss is common?

What is conductive bilateral hearing loss?


300

While hearing loss is not a defining feature, audiologic care is recommended due to be what nature of PHACES?

What is delayed or progressive
300

These are the most common factor associated

What is Genetic, Environmental, and structural abnormality

400

This complication is believed to result from what?

What is cholera ischemia Bonus: +200 What is labryinthine artery occlusion? 

400

This is a audiologic diagnosis that can often be similar to or seen in children with ASD

What is Auditory Processing Disorder OR Hard of Hearing/ Deaf

400

What is the percentage in pediatric cases that have otologic involvement? 

What is 40-70 percent

400

Audiologic findings are usually found where compared to associated anomalies and imaging?


What is unilateral and ipsilateral 

400

Of the following, this treatment should be immediately switched if a response is not noted. Anti-epileptic, anti-seizure, steroids, psychostimulants

What is antiepileptic medication

500

A patient with a history SCD reports a history of stroke, anemia, acute chest syndrome, acute chest syndrome, and priapism. What other symptoms/ dysfunction may they experience?

What is hypogonadism or infertility

500

These are the deficits classified by the DSM-V for ASD

What is deficits in nonverbal communication behaviors, social-emotional reciprocity, and developing, maintaining and understanding relationships

Bonus +50 what his 2 repetitive pattern behaviors

500

A patient with this condition comes to the clinic, their parent states they have experienced chronic otorrhea, behavioral changes, and hearing, speech, and behavioral concerns. Which of these is considered the high risk indicator?

What is patient concern. 

500

The three reported mechanisms impacting audiologic findings include external/middle ear involvement, intracranial lesions affecting the auditory pathway and what?

What is temporal bone abnormalities

500

Of the associated symptoms, this symptom is known to resolve by what time period?

What is seizures and adolescence