Usher & Hearing
Usher & Vision
Types of Usher Syndrome
Audiogram Application
Screening
100

A hearing loss in the outer or middle ear where the sound cannot reach the hearing nerve.

What is conductive hearing loss?

100

The type of vision loss known for a narrowing field of vision and is present in all students with Usher Syndrome.

What is retinitis pigmentosa?

100

Type of Usher syndrome when night blindness begins in the teens and tunnel vision begins in the late teens into early adulthood.

What is Type II Usher Syndrome?

100

An type of audiological report that depicts this indicates a conductive loss and the student does not need to be screened.

What is an air vs. bone gap greater than 20 dB.

100

These are the three questionnaires that must be completed if the student was not eliminated during the cumulative file review.

What are the Family History Questionnaire, Visual and Motor Behavior Questionnaire and Student Questionnaire?

100

A hearing loss that occurs in the inner ear, the auditory nerve that runs from the cochlea to the brain or within the brain and is permanent.

What is a sensorineural hearing loss?

100

This visual ability deteriorates first in usher syndrome.

What is the ability to see in dim light?

100

The type of Usher syndrome where a child is born with profound hearing loss in both ears and the visual field loss is typically detected in early elementary years.

What is Type I Usher syndrome?

100

These are the first 2 steps in screening for Usher syndrome.

What are reviewing the cumulative file and audiogram?

100

This is what must accompany the Family History Questionnaire to inform the family of your intent.

What is a letter of notification?

100

A hearing loss that is a combination of a sensorineural and conductive.

What is a mixed hearing loss?

100
The term that is used to describe a person who has an acuity of 20/200 or less in the best corrected eye, or a field loss of 20 degrees or less.

What is legally blind?

100

The type of Usher syndrome that is characterized by the late onset of sensorineural hearing loss and late onset of retinitis pigmentosa without vestibular involvement.

What is Type IV Usher syndrome?

100

This is what you do if the audiogram does fall in line with audiograms associated with Usher syndrome.

What is file a letter in the cumulative folder describing the review and findings of the audiogram?

100

This is what you do after determining the student is at low risk.

What is stop the screening process and add a letter to the cumulative folder with the audiogram?

100
A hearing test where the results are reported using the symbols [ and ].  

What is bone conduction?

100

A condition characterized by clouding of the lens that typically develops later in life.

What are cataracts?

100

The common milestone that children with Type I Usher syndrome are commonly late to develop due to balance issues.

What is walking?

100

This is what you should do going forward if a child's audiogram has a slope but they do not show other symptoms during the initial testing.

What is complete on-site screening annually until you identify Usher syndrome or you rule it out?

100

These are the people wo complete the Visual and Motor Behavior Questionnaire.

Who are the educational service providers familiar with the student?

100

The symbol represents thresholds on a hearing test for the right ear.

What is O?

100

The typical visual field when using peripheral vision.

What is 175 degrees?

100

This type of Usher Syndrome is represented by a sloping hearing loss that becomes worse over time.

Type III

100

This is the type of screening you complete if a student has an audiogram indicative of Usher syndrome.

What is a paper screening?

100

This is what you do if you determine the student is high risk.

What is Continue with on-site screening?